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TITLE: Expert Consensus on the Long-Term Effectiveness of Medical Nutrition Therapy and Its Impact on the Outcomes of Adults with Phenylketonuria  Full Text
AUTHORS: Rocha, Julio Cesar ; Ahring, Kirsten K.; Bausell, Heather; Bilder, Deborah A.; Harding, Cary O.; Inwood, Anita; Longo, Nicola; Muntau, Ania C.; Pessoa, Andre L. Santos; Rohr, Fran; Sivri, Serap; Hermida, Alvaro;
PUBLISHED: 2023, SOURCE: NUTRIENTS, VOLUME: 15, ISSUE: 18
INDEXED IN: Scopus WOS
2
TITLE: Impact on Diet Quality and Burden of Care in Sapropterin Dihydrochloride Use in Children with Phenylketonuria: A 6 Month Follow-Up Report  Full Text
AUTHORS: Gama, Maria Ines; Daly, Anne; Ashmore, Catherine; Evans, Sharon; Moreira Rosario, Andre ; Rocha, Julio Cesar ; MacDonald, Anita;
PUBLISHED: 2023, SOURCE: NUTRIENTS, VOLUME: 15, ISSUE: 16
INDEXED IN: Scopus WOS CrossRef
3
TITLE: Phenylalanine Tolerance over Time in Phenylketonuria: A Systematic Review and Meta-Analysis  Full Text
AUTHORS: Pinto, Alex; Ilgaz, Fatma; Evans, Sharon; van Dam, Esther; Rocha, Julio Cesar ; Karabulut, Erdem; Hickson, Mary; Daly, Anne; MacDonald, Anita;
PUBLISHED: 2023, SOURCE: NUTRIENTS, VOLUME: 15, ISSUE: 16
INDEXED IN: Scopus WOS
4
TITLE: Preliminary Data on Free Use of Fruits and Vegetables Containing Phenylalanine 76-100 mg/100 g of Food in 16 Children with Phenylketonuria: 6 Months Follow-Up  Full Text
AUTHORS: Pinto, Alex; Daly, Anne; Rocha, Julio Cesar ; Ashmore, Catherine; Evans, Sharon; Jackson, Richard; Hickson, Mary; MacDonald, Anita;
PUBLISHED: 2023, SOURCE: NUTRIENTS, VOLUME: 15, ISSUE: 13
INDEXED IN: Scopus WOS
5
TITLE: Total Protein Intake in Patients with PKU: Adequacy Evaluation According to the European PKU Guidelines from 2017  Full Text
AUTHORS: Gomes, Melanie; Almeida, Manuela Ferreira ; Barbosa, Catarina Sousa; Gama, Maria Ines; Peres, Maria; Pinto, Elia; Macdonald, Anita; Rocha, Julio Cesar ;
PUBLISHED: 2023, SOURCE: NUTRIENTS, VOLUME: 15, ISSUE: 23
INDEXED IN: Scopus WOS
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TITLE: Trimethylamine increases intestinal fatty acid absorption: in vitro studies in a Caco-2 cell culture system  Full Text
AUTHORS: Rodrigues, Catarina; Ismael, Shamila; Castela, Ines; Barreiros Mota, Ines; Almeida, Maria Joao; Santos, Gilberto Maia; Calhau, Conceicao ; Rocha, Julio Cesar ; Faria, Ana ; Araujo, Joao R.;
PUBLISHED: 2023, SOURCE: JOURNAL OF NUTRITIONAL SCIENCE, VOLUME: 12
INDEXED IN: Scopus WOS
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TITLE: A Three-Year Longitudinal Study Comparing Bone Mass, Density, and Geometry Measured by DXA, pQCT, and Bone Turnover Markers in Children with PKU Taking L-Amino Acid or Glycomacropeptide Protein Substitutes  Full Text
AUTHORS: Daly, A; Hogler, W; Crabtree, N; Shaw, N; Evans, S; Pinto, A; Jackson, R; Ashmore, C; Rocha, JC ; Strauss, BJ; Wilcox, G; Fraser, WD; Tang, JCY; MacDonald, A;
PUBLISHED: 2021, SOURCE: NUTRIENTS, VOLUME: 13, ISSUE: 6
INDEXED IN: Scopus WOS
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TITLE: Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective  Full Text
AUTHORS: Pena, MJ; Pinto, A; de Almeida, MF; Barbosa, CD; Ramos, PC; Rocha, S; Guimas, A; Ribeiro, R; Martins, E; Bandeira, A; Dias, CC; MacDonald, A; Borges, N ; Rocha, JC ;
PUBLISHED: 2021, SOURCE: ORPHANET JOURNAL OF RARE DISEASES, VOLUME: 16, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 11
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TITLE: Development of a practical dietitian road map for the nutritional management of phenylketonuria (PKU) patients on pegvaliase
AUTHORS: Rocha, JC ; Bausell, H; Belanger Quintana, A; Bernstein, L; Gokmen Ozel, H; Jung, A; MacDonald, A; Rohr, F; van Dam, E; Heddrich Ellerbrok, M;
PUBLISHED: 2021, SOURCE: MOLECULAR GENETICS AND METABOLISM REPORTS, VOLUME: 28
INDEXED IN: Scopus WOS
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TITLE: Growth and Body Composition in PKU Children-A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes  Full Text
AUTHORS: Daly, A; Hogler, W; Crabtree, N; Shaw, N; Evans, S; Pinto, A; Jackson, R; Strauss, BJ; Wilcox, G; Rocha, JC ; Ashmore, C; MacDonald, A;
PUBLISHED: 2021, SOURCE: NUTRIENTS, VOLUME: 13, ISSUE: 4
INDEXED IN: Scopus WOS
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