11
TITLE: Mutant Ataxin-2 Expression in Aged Animals Aggravates Neuropathological Features Associated with Spinocerebellar Ataxia Type 2
AUTHORS: Afonso, Ines T.; Lima, Patricia; Conceicao, Andre; Matos, Carlos A.; Nobrega, Clevio ;
PUBLISHED: 2022, SOURCE: INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, VOLUME: 23, ISSUE: 19
INDEXED IN: Scopus WOS CrossRef: 1
12
TITLE: p ULK overexpression mitigates motor deficits and neuropathology in mouse models of Machado-Joseph disease
AUTHORS: Vasconcelos Ferreira, A; Martins, IM; Lobo, D; Pereira, D; Lopes, MM; Faro, R; Lopes, SM; Verbeek, D; Schmidt, T; Nobrega, C ; de Almeida, LP ;
PUBLISHED: 2022, SOURCE: MOLECULAR THERAPY, VOLUME: 30, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 10
13
TITLE: The stress granule protein G3BP1 alleviates spinocerebellar ataxia-associated deficits
AUTHORS: Koppenol, Rebekah; Conceicao, Andre; Afonso, Ines T.; Afonso Reis, Ricardo; Costa, Rafael G.; Tome, Sandra; Teixeira, Diogo; da Silva, Joana Pinto; Codesso, Jose Miguel; Brito, David V. C.; Mendonca, Liliana; Marcelo, Adriana; de Almeida, Luis Pereira ; Matos, Carlos A.; Nobrega, Clevio ;
PUBLISHED: 2022, SOURCE: BRAIN, VOLUME: 146, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 12
14
TITLE: Autophagy in Spinocerebellar ataxia type 2, a dysregulated pathway, and a target for therapy  Full Text
AUTHORS: Marcelo, A; Afonso, IT; Afonso Reis, R; Brito, DVC; Costa, RG; Rosa, A; Alves Cruzeiro, J; Ferreira, B; Henriques, C; Nobre, RJ ; Matos, CA; De Almeida, LP ; Nobrega, C ;
PUBLISHED: 2021, SOURCE: Cell Death and Disease in CELL DEATH & DISEASE, VOLUME: 12, ISSUE: 12
INDEXED IN: Scopus WOS CrossRef: 19 Handle
15
TITLE: Current Status of Gene Therapy Research in Polyglutamine Spinocerebellar Ataxias
AUTHORS: Afonso Reis, R; Afonso, IT; Nobrega, C ;
PUBLISHED: 2021, SOURCE: INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, VOLUME: 22, ISSUE: 8
INDEXED IN: Scopus WOS CrossRef: 15
16
TITLE: Stress granules, RNA-binding proteins and polyglutamine diseases: too much aggregation?
AUTHORS: Marcelo, A; Koppenol, R; de Almeida, LP ; Matos, CA; Nobrega, C ;
PUBLISHED: 2021, SOURCE: CELL DEATH & DISEASE, VOLUME: 12, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 94
17
TITLE: The autophagy-enhancing drug carbamazepine improves neuropathology and motor impairment in mouse models of Machado-Joseph disease  Full Text
AUTHORS: Vasconcelos Ferreira, A; Carmo Silva, S; Codesso, JM; Silva, P; Martinez, ARM; Franca, MC; Nobrega, C ; de Almeida, LP ;
PUBLISHED: 2021, SOURCE: Neuropathology and Applied Neurobiology in NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY, VOLUME: 48, ISSUE: 1
INDEXED IN: WOS CrossRef: 17 Handle
18
TITLE: The cholesterol 24-hydroxylase activates autophagy and decreases mutant huntingtin build-up in a neuroblastoma culture model of Huntington's disease
AUTHORS: Nóbrega, C ; Conceição, A; Costa, RG; Koppenol, R; Sequeira, RL; Nunes, R; Carmo Silva, S; Marcelo, A; Matos, CA; Betuing, S; Caboche, J; Cartier, N; Alves, S;
PUBLISHED: 2020, SOURCE: BMC research notes, VOLUME: 13, ISSUE: 1
INDEXED IN: Scopus CrossRef: 11
19
TITLE: Trehalose alleviates the phenotype of Machado-Joseph disease mouse models  Full Text
AUTHORS: Santana, MM; Paixao, S; Cunha Santos, J; Silva, TP; Trevino Garcia, A; Gaspar, LS; Nobrega, C ; Nobre, RJ ; Cavadas, C ; Greif, H; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: JOURNAL OF TRANSLATIONAL MEDICINE, VOLUME: 18, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 23
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TITLE: Cordycepin activates autophagy through AMPK phosphorylation to reduce abnormalities in Machado-Joseph disease models
AUTHORS: Marcelo, A; Brito, F; Carmo Silva, S; Matos, CA; Alves Cruzeiro, J; Vasconcelos Ferreira, A; Koppenol, R; Mendonca, L; de Almeida, LP ; Nobrega, C ;
PUBLISHED: 2019, SOURCE: HUMAN MOLECULAR GENETICS, VOLUME: 28, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 37
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