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TITLE: Cholesterol redistribution triggered by CYP46A1 gene therapy improves major hallmarks of Niemann-Pick type C disease but is not sufficient to halt neurodegeneration  Full Text
AUTHORS: Nunes, Maria Joao; Carvalho, Andreia Neves; Reis, Joana; Costa, Daniela; Moutinho, Miguel; Mateus, Joana; de Almeida, Rita Mendes; Brito, Sara; Risso, Daniela; Nunes, Sofia; Castro Caldas, Margarida; Gama, Maria Joa ; Rodrigues, Cecilia M. P. ; Xapelli, Sara ; Diogenes, Maria Jose ; Cartier, Nathalie; Chali, Farah; Piguet, Francoise; Rodrigues, Elsa;
PUBLISHED: 2024, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1870, ISSUE: 3
INDEXED IN: Scopus WOS CrossRef
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TITLE: Glucocorticoid receptor-dependent therapeutic efficacy of tauroursodeoxycholic acid in preclinical models of spinocerebellar ataxia type 3
AUTHORS: Sara Duarte-Silva; Jorge Diogo Da Silva; Daniela Monteiro-Fernandes; Marta Daniela Costa; Andreia Neves-Carvalho; Mafalda Raposo; Carina Soares-Cunha; Joana S Correia; Gonçalo Nogueira-Goncalves; Henrique S Fernandes; Stephanie Oliveira; Ana Rita Ferreira-Fernandes; Fernando Rodrigues; Joana Pereira-Sousa; Daniela Vilasboas-Campos; Sara Guerreiro; Jonas Campos; Liliana Meireles-Costa; Cecilia M.P Rodrigues ; Stephanie Cabantous; Sergio F Sousa; Manuela Lima ; Andreia Teixeira-Castro; Patricia Maciel ; ...More
PUBLISHED: 2024, SOURCE: Journal of Clinical Investigation, VOLUME: 134, ISSUE: 5
INDEXED IN: CrossRef
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TITLE: NPC1-like phenotype, with intracellular cholesterol accumulation and altered mTORC1 signaling in models of Parkinson's disease  Full Text
AUTHORS: Caria, Ines; Nunes, Maria Joao; Ciraci, Viviana; Carvalho, Andreia Neves; Ranito, Catarina; Santos, Susana G.; Gama, Maria Joao ; Castro Caldas, Margarida; Rodrigues, Cecilia M. P. ; Ruas, Jorge L.; Rodrigues, Elsa;
PUBLISHED: 2024, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1870, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef: 2
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TITLE: Sustained PGC-1α2 or PGC-1α3 expression induces astrocyte dysfunction and degeneration  Full Text
AUTHORS: Nunes, M. J.; Carvalho, A. N.; Sa Lemos, C.; Colaco, M.; Cervenka, I.; Ciraci, V.; Santos, S. G.; Ribeiro, M. M.; Castanheira, M.; Jannig, P. R.; Gama, M. J. ; Castro Caldas, M.; Rodrigues, C. M. P. ; Rodrigues, E.; Ruas, J. L.;
PUBLISHED: 2024, SOURCE: EUROPEAN JOURNAL OF CELL BIOLOGY, VOLUME: 103, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 1
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TITLE: A step forward on the in vitro and in vivo assessment of a novel nanomedicine against melanoma  Full Text
AUTHORS: Pinho, Jacinta O.; Matias, Mariana; Godinho Santos, Ana; Amaral, Joana D.; Mendes, Eduarda; Perry, Maria Jesus; Francisco, Ana Paula; Rodrigues, Cecilia M. P. ; Gaspar, M. Manuela ;
PUBLISHED: 2023, SOURCE: INTERNATIONAL JOURNAL OF PHARMACEUTICS, VOLUME: 640
INDEXED IN: Scopus WOS CrossRef: 4
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TITLE: Apoptosis-50 Years after Its Discovery
AUTHORS: Capela e Silva, Fernando; Rodrigues, Cecilia M. P. ;
PUBLISHED: 2023, SOURCE: BIOMEDICINES, VOLUME: 11, ISSUE: 4
INDEXED IN: Scopus WOS CrossRef: 4
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TITLE: ARBM101 (Methanobactin SB2) Drains Excess Liver Copper via Biliary Excretion in Wilson's Disease Rats
AUTHORS: Einer, Claudia; Munk, Ditte Emilie; Park, Eok; Akdogan, Banu; Nagel, Judith; Lichtmannegger, Josef; Eberhagen, Carola; Rieder, Tamara; Vendelbo, Mikkel H.; Michalke, Bernhard; Wimmer, Ralf; Blutke, Andreas; Feuchtinger, Annette; Dershwitz, Philip; DiSpirito, Ana M.; Islam, Tawhidul; Castro, Rui E.; Min, Byong Keol; Kim, TaeWon; Choi, Seoyoun; Kim, Dasol; Jung, Chunwon; Lee, Hongjae; Park, Dongsik; Im, Weonbin; Eun, So Young; Cho, You Hee; Semrau, Jeremy D.; Rodrigues, Cecilia M. P. ; Hohenester, Simon; Sandahl, Thomas Damgaard; DiSpirito, Alan A.; Zischka, Hans; ...More
PUBLISHED: 2023, SOURCE: GASTROENTEROLOGY, VOLUME: 165, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 14
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TITLE: Comparative Chemical Profiling and Antimicrobial/Anticancer Evaluation of Extracts from Farmed versus Wild Agelas oroides and Sarcotragus foetidus Sponges  Full Text
AUTHORS: Despoina Varamogianni-Mamatsi; Maria João Nunes; Vanda Marques; Thekla I Anastasiou; Eirini Kagiampaki; Emmanouela Vernadou; Thanos Dailianis; Nicolas Kalogerakis; Luís C Branco; Cecília M P Rodrigues ; Rita G Sobral; Susana P Gaudêncio; Manolis Mandalakis;
PUBLISHED: 2023, SOURCE: Marine Drugs, VOLUME: 21, ISSUE: 12
INDEXED IN: CrossRef
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TITLE: Decoding the role of leptin and adiponectin in obesity-related gastrointestinal cancer
AUTHORS: Marques, Vanda; Arella, Fabiola; Afonso, Marta B.; Santos, Andre A.; Rodrigues, Cecilia M. P. ;
PUBLISHED: 2023, SOURCE: CLINICAL SCIENCE, VOLUME: 137, ISSUE: 15
INDEXED IN: Scopus WOS CrossRef: 1
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TITLE: Human liver organoids: From generation to applications  Full Text
AUTHORS: Afonso, Marta B.; Marques, Vanda; van Mil, Saskia W. C.; Rodrigues, Cecilia M. P. ;
PUBLISHED: 2023, SOURCE: HEPATOLOGY, VOLUME: 79, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 3
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