Margarida Maria Fernandes Baptista Silva
AuthID: R-000-ADY
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TITLE: Valproyl-CoA inhibits the activity of ATP- and GTP-dependent succinate:CoA ligases Full Text
AUTHORS: Paula B M Luís; Jos Ruiter; Lodewijk IJlst; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2013, SOURCE: Journal of Inherited Metabolic Disease - J Inherit Metab Dis
AUTHORS: Paula B M Luís; Jos Ruiter; Lodewijk IJlst; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2013, SOURCE: Journal of Inherited Metabolic Disease - J Inherit Metab Dis
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TITLE: Free fatty acids and acylcarnitines profiling in rat to elucidate drug-induced steatosis Full Text
AUTHORS: Moedas, MF; Luis, PBM; Ijlst, L; van Lenthe, H; Duran, M; de Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2012, SOURCE: 22nd IUBMB Congress/37th FEBS Congress in FEBS JOURNAL, VOLUME: 279
AUTHORS: Moedas, MF; Luis, PBM; Ijlst, L; van Lenthe, H; Duran, M; de Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2012, SOURCE: 22nd IUBMB Congress/37th FEBS Congress in FEBS JOURNAL, VOLUME: 279
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TITLE: LIVER ACYLCARNITINES IN RATS UNDER ACUTE AND SUBCHRONIC TREATMENT WITH SODIUM VALPROATE
AUTHORS: Luis, PBM; IJlst, L; van Lenthe, H; Duran, M; Tavares de Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
AUTHORS: Luis, PBM; IJlst, L; van Lenthe, H; Duran, M; Tavares de Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
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TITLE: A STABLE ISOTOPE DILUTION GC/MS METHOD FOR THE NANOMOLAR RANGE DETERMINATION OF METHYLMALONIC ACID IN BIOLOGICAL FLUIDS
AUTHORS: Moedas, MF; Ramos, R; Pinto, R; Silva, MFB; Struys, EA; Tavares de Almeida, IT;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
AUTHORS: Moedas, MF; Ramos, R; Pinto, R; Silva, MFB; Struys, EA; Tavares de Almeida, IT;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
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TITLE: Inhibition of 3-methylcrotonyl-CoA carboxylase explains the increased excretion of 3-hydroxyisovaleric acid in valproate-treated patients Full Text
AUTHORS: Paula B M Luís; Jos P Ruiter; Lodewijk IJlst; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F B Silva;
PUBLISHED: 2011, SOURCE: Journal of Inherited Metabolic Disease - J Inherit Metab Dis, VOLUME: 35, ISSUE: 3
AUTHORS: Paula B M Luís; Jos P Ruiter; Lodewijk IJlst; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F B Silva;
PUBLISHED: 2011, SOURCE: Journal of Inherited Metabolic Disease - J Inherit Metab Dis, VOLUME: 35, ISSUE: 3
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TITLE: Valproic acid utilizes the isoleucine breakdown pathway for its complete β-oxidation Full Text
AUTHORS: Paula B.M Luís; Jos P Ruiter; Rob Ofman; Lodewijk IJlst; Marco Moedas; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F.B Silva;
PUBLISHED: 2011, SOURCE: Biochemical Pharmacology, VOLUME: 82, ISSUE: 11
AUTHORS: Paula B.M Luís; Jos P Ruiter; Rob Ofman; Lodewijk IJlst; Marco Moedas; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F.B Silva;
PUBLISHED: 2011, SOURCE: Biochemical Pharmacology, VOLUME: 82, ISSUE: 11
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TITLE: Influence of valproate on the levels of tri- and diphosphate nucleotides in rat liver tissues Full Text
AUTHORS: Paula B M Luis; Lodewijk Ijlst; Jeroen Roelofsen; Andre B P van Kuilenburg; Marinus Duran; Isabel Tavares de Almeida; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2010, SOURCE: 9th International Meeting of the International-Society-for-the-Study-of-Xenobiotics(ISSX) in DRUG METABOLISM REVIEWS, VOLUME: 42
AUTHORS: Paula B M Luis; Lodewijk Ijlst; Jeroen Roelofsen; Andre B P van Kuilenburg; Marinus Duran; Isabel Tavares de Almeida; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2010, SOURCE: 9th International Meeting of the International-Society-for-the-Study-of-Xenobiotics(ISSX) in DRUG METABOLISM REVIEWS, VOLUME: 42
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TITLE: INFLUENCE OF SODIUM VALPROATE ON THE HOMEOSTASIS OF HEPATIC FREE COENZYME A Full Text
AUTHORS: Luis, PBM; IJlst, L; van Cruchten, A; Duran, M; Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2010, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 33
AUTHORS: Luis, PBM; IJlst, L; van Cruchten, A; Duran, M; Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2010, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 33
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TITLE: VALPROATE INHIBITS THE ACTIVITY OF ATP- AND GTP-DEPENDENT SUCCINYL-CoA SYNTHETASE Full Text
AUTHORS: Luis, PBM; Ruiter, J; IJlst, L; Duran, M; Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2010, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 33
AUTHORS: Luis, PBM; Ruiter, J; IJlst, L; Duran, M; Almeida, IT; Wanders, RJA; Silva, MFB;
PUBLISHED: 2010, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 33
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TITLE: BIOSYNTHESIS OF VALPROYLCARNITINE: A PUZZLING REACTION IN VITRO VERSUS IN VIVO Full Text
AUTHORS: Aires, CCP; van Lenthe, H; Ijlst, L; Ruiter, J; Minkler, P; Hoppel, CL; Tavares T de Almeida; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2009, SOURCE: 11th International Conference of Inborn Errors of Metabolism in MOLECULAR GENETICS AND METABOLISM, VOLUME: 98, ISSUE: 1-2
AUTHORS: Aires, CCP; van Lenthe, H; Ijlst, L; Ruiter, J; Minkler, P; Hoppel, CL; Tavares T de Almeida; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2009, SOURCE: 11th International Conference of Inborn Errors of Metabolism in MOLECULAR GENETICS AND METABOLISM, VOLUME: 98, ISSUE: 1-2
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