Margarida Maria Fernandes Baptista Silva
AuthID: R-000-ADY
31
TITLE: Quantitative analysis of N-acetylglutamate and orotic acid by MS-MS: underlying mechanism of valproate effect on mitochondrial detoxification of ammonia Full Text
AUTHORS: Aires, C; van Cruchten, A; Ruiter, J; Ijlst, L; Tavares T de Almeida; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2009, SOURCE: 34th Congress of the Federation-of-European-Biochemical-Societies in FEBS JOURNAL, VOLUME: 276
AUTHORS: Aires, C; van Cruchten, A; Ruiter, J; Ijlst, L; Tavares T de Almeida; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2009, SOURCE: 34th Congress of the Federation-of-European-Biochemical-Societies in FEBS JOURNAL, VOLUME: 276
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32
TITLE: Potential interference of valproic acid with the biotin-dependent carboxylase of leucine metabolism Full Text
AUTHORS: Luis, P; Tavares T de Almeida; Silva, MFB; Ruiter, JP; Ijlst, L; Duran, M; Wanders, RJA; Diogo, L; Garcia, P;
PUBLISHED: 2009, SOURCE: 34th Congress of the Federation-of-European-Biochemical-Societies in FEBS JOURNAL, VOLUME: 276
AUTHORS: Luis, P; Tavares T de Almeida; Silva, MFB; Ruiter, JP; Ijlst, L; Duran, M; Wanders, RJA; Diogo, L; Garcia, P;
PUBLISHED: 2009, SOURCE: 34th Congress of the Federation-of-European-Biochemical-Societies in FEBS JOURNAL, VOLUME: 276
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33
TITLE: Hyperammonemia Induced by Valproic Acid Therapy: Urea Cycle Impairment by Intramitochondrial Valproyl-CoA Full Text
AUTHORS: Catia C P Aires; Arno van Cruchten; Jos Ruiter; Lodewijk Ijlst; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2009, SOURCE: 11th European Regional ISSX Meeting in DRUG METABOLISM REVIEWS, VOLUME: 41
AUTHORS: Catia C P Aires; Arno van Cruchten; Jos Ruiter; Lodewijk Ijlst; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2009, SOURCE: 11th European Regional ISSX Meeting in DRUG METABOLISM REVIEWS, VOLUME: 41
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34
TITLE: Toward the Complete Elucidation of the Mitochondrial beta-Oxidation Pathway of Valproic Acid and its Interference with the Oxidation of Branched-Chain Amino Acids Full Text
AUTHORS: Paula B M Luis; Jos Ruiter; Lodewijk Ijlst; Rob Ofman; Luisa Diogo; Paula Garcia; Marinus Duran; Jerry Vockley; Isabel Tavares de Almeida; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2009, SOURCE: 11th European Regional ISSX Meeting in DRUG METABOLISM REVIEWS, VOLUME: 41
AUTHORS: Paula B M Luis; Jos Ruiter; Lodewijk Ijlst; Rob Ofman; Luisa Diogo; Paula Garcia; Marinus Duran; Jerry Vockley; Isabel Tavares de Almeida; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2009, SOURCE: 11th European Regional ISSX Meeting in DRUG METABOLISM REVIEWS, VOLUME: 41
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35
TITLE: The Portuguese pharmaceutical market in the near future - A time series exploration approach Full Text
AUTHORS: Baptista, MHMF; Mendes, JM ;
PUBLISHED: 2009, SOURCE: Journal of Medical Marketing, VOLUME: 9, ISSUE: 4
AUTHORS: Baptista, MHMF; Mendes, JM ;
PUBLISHED: 2009, SOURCE: Journal of Medical Marketing, VOLUME: 9, ISSUE: 4
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CrossRef36
TITLE: 3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: Initial presentation in a young adult
AUTHORS: Reimao, S; Morgado, C; Almeida, IT; Silva, M; Real, HC; Campos, J;
PUBLISHED: 2009, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 32, ISSUE: 1
AUTHORS: Reimao, S; Morgado, C; Almeida, IT; Silva, M; Real, HC; Campos, J;
PUBLISHED: 2009, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 32, ISSUE: 1
37
TITLE: Mechanisms of valproic acid toxicity: Studies on acyl-CoA interference with the urea cycle Full Text
AUTHORS: Catia C P Aires; Arno van Cruchten; Jos Ruiter; Lodewijk Ijist; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2008, SOURCE: 45th Congress of the European-Societies-of-Toxicology in TOXICOLOGY LETTERS, VOLUME: 180
AUTHORS: Catia C P Aires; Arno van Cruchten; Jos Ruiter; Lodewijk Ijist; Isabel Tavares de Almeida; Marinus Duran; Ronald J A Wanders; Margarida F B Silva;
PUBLISHED: 2008, SOURCE: 45th Congress of the European-Societies-of-Toxicology in TOXICOLOGY LETTERS, VOLUME: 180
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38
TITLE: Interference of valproic acid on the branched chain amino acid oxidative metabolism Full Text
AUTHORS: Luis, PBM; Ruiter, JPN; Ijlst, L; Ofman, R; Diogo, L; Garcia, P; Duran, M; Vockley, J; de Almeida Travares; Wanders, RJA; Silva, MFB;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
AUTHORS: Luis, PBM; Ruiter, JPN; Ijlst, L; Ofman, R; Diogo, L; Garcia, P; Duran, M; Vockley, J; de Almeida Travares; Wanders, RJA; Silva, MFB;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
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39
TITLE: Molecular analysis of medium-chain acyl-CoA dehydrogenase deficiency in Portugal Full Text
AUTHORS: Luz, A; Violante, S; Gaspar, A; Antunes M Lobo; Rivera, IA; Silva, MFB; Ramos, A; Rocha, H; Sousa, C; Marcao, A; Fonseca, H; Ventura, FV; Leandro, P ; Vilarinho, L; de Almeida Tavares;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
AUTHORS: Luz, A; Violante, S; Gaspar, A; Antunes M Lobo; Rivera, IA; Silva, MFB; Ramos, A; Rocha, H; Sousa, C; Marcao, A; Fonseca, H; Ventura, FV; Leandro, P ; Vilarinho, L; de Almeida Tavares;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
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40
TITLE: Inhibition of N-acetyl-glutamate synthase activity in valproate-associated hyperammonemia Full Text
AUTHORS: Aires, CCP; van Cruchten, A; Ruiter, J; Ijlst, L; De Almeida Tavares; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
AUTHORS: Aires, CCP; van Cruchten, A; Ruiter, J; Ijlst, L; De Almeida Tavares; Duran, M; Wanders, RJA; Silva, MFB;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
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