Margarida Sofia Pereira Duarte Amaral
AuthID: R-000-AER
41
TITLE: Human epididymis protein 4 (HE4) levels inversely correlate with lung function improvement (delta FEV1) in cystic fibrosis patients receiving ivacaftor treatment Full Text
AUTHORS: Bela Nagy; Zsolt Bene; Zsolt Fejes; Sonya L Heltshe; David Reid; Nicola J Ronan; Yvonne McCarthy; Daniel Smith; Attila Nagy; Elizabeth Joseloff; Gyorgy Balla; Janos Kappelmayer; Milan Macek; Scott C Bell; Barry J Plant; Margarida D Amaral; Istvan Balogh;
PUBLISHED: 2019, SOURCE: JOURNAL OF CYSTIC FIBROSIS, VOLUME: 18, ISSUE: 2
AUTHORS: Bela Nagy; Zsolt Bene; Zsolt Fejes; Sonya L Heltshe; David Reid; Nicola J Ronan; Yvonne McCarthy; Daniel Smith; Attila Nagy; Elizabeth Joseloff; Gyorgy Balla; Janos Kappelmayer; Milan Macek; Scott C Bell; Barry J Plant; Margarida D Amaral; Istvan Balogh;
PUBLISHED: 2019, SOURCE: JOURNAL OF CYSTIC FIBROSIS, VOLUME: 18, ISSUE: 2
INDEXED IN: Scopus WOS
42
TITLE: Insights into the population structure and pan-genome of Haemophilus influenzae Full Text
AUTHORS: Pinto, M; Gonzalez Diaz, A; Machado, MP; Duarte, S; Vieira, L; Carrico, JA; Marti, S; Bajanca Lavado, MP; Gomes, JP;
PUBLISHED: 2019, SOURCE: INFECTION GENETICS AND EVOLUTION, VOLUME: 67
AUTHORS: Pinto, M; Gonzalez Diaz, A; Machado, MP; Duarte, S; Vieira, L; Carrico, JA; Marti, S; Bajanca Lavado, MP; Gomes, JP;
PUBLISHED: 2019, SOURCE: INFECTION GENETICS AND EVOLUTION, VOLUME: 67
INDEXED IN: Scopus WOS
43
TITLE: The effect of premature termination codon mutations on CFTR mRNA abundance in human nasal epithelium and intestinal organoids: a basis for read-through therapies in cystic fibrosis Full Text
AUTHORS: Luka A Clarke; Nikhil T Awatade; Veronica M Felicio; Iris A Silva; Maite Calucho; Luisa Pereira; Pilar Azevedo; Jose Cavaco; Celeste Barreto; Carmen Bertuzzo; Silvia Gartner; Jeffrey Beekman; Margarida D Amaral;
PUBLISHED: 2019, SOURCE: HUMAN MUTATION, VOLUME: 40, ISSUE: 3
AUTHORS: Luka A Clarke; Nikhil T Awatade; Veronica M Felicio; Iris A Silva; Maite Calucho; Luisa Pereira; Pilar Azevedo; Jose Cavaco; Celeste Barreto; Carmen Bertuzzo; Silvia Gartner; Jeffrey Beekman; Margarida D Amaral;
PUBLISHED: 2019, SOURCE: HUMAN MUTATION, VOLUME: 40, ISSUE: 3
INDEXED IN: Scopus WOS
44
TITLE: Increases in cytosolic Ca2+ induce dynamin- and calcineurin-dependent internalisation of CFTR Full Text
AUTHORS: Waseema Patel; Patrick J Moore; Flori F Sassano; Miqueias Lopes Pacheco; Andrei A Aleksandrov; Margarida D Amaral; Robert Tarran; Michael A Gray;
PUBLISHED: 2019, SOURCE: CELLULAR AND MOLECULAR LIFE SCIENCES, VOLUME: 76, ISSUE: 5
AUTHORS: Waseema Patel; Patrick J Moore; Flori F Sassano; Miqueias Lopes Pacheco; Andrei A Aleksandrov; Margarida D Amaral; Robert Tarran; Michael A Gray;
PUBLISHED: 2019, SOURCE: CELLULAR AND MOLECULAR LIFE SCIENCES, VOLUME: 76, ISSUE: 5
INDEXED IN: Scopus WOS
45
TITLE: Research ethics in palliative care: A hallmark in Palliative Medicine
AUTHORS: Pereira, SM; Hernández Marrero, P;
PUBLISHED: 2019, SOURCE: Palliative Medicine
AUTHORS: Pereira, SM; Hernández Marrero, P;
PUBLISHED: 2019, SOURCE: Palliative Medicine
INDEXED IN: Scopus
46
TITLE: CFTR modulator theratyping: Current status, gaps and future directions Full Text
AUTHORS: John Paul Clancy; Calvin U Cotton; Scott H Donaldson; George M Solomon; Donald R VanDevanter; Michael P Boyle; Martina Gentzsch; Jerry A Nick; Beate Illek; John C Wallenburg; Eric J Sorscher; Margarida D Amaral; Jeffrey M Beekman; Anjaparavanda P Naren; Robert J Bridges; Philip J Thomas; Garry Cutting; Steven Rowe; Anthony G Durmowicz; Martin Mense; ...More
PUBLISHED: 2019, SOURCE: JOURNAL OF CYSTIC FIBROSIS, VOLUME: 18, ISSUE: 1
AUTHORS: John Paul Clancy; Calvin U Cotton; Scott H Donaldson; George M Solomon; Donald R VanDevanter; Michael P Boyle; Martina Gentzsch; Jerry A Nick; Beate Illek; John C Wallenburg; Eric J Sorscher; Margarida D Amaral; Jeffrey M Beekman; Anjaparavanda P Naren; Robert J Bridges; Philip J Thomas; Garry Cutting; Steven Rowe; Anthony G Durmowicz; Martin Mense; ...More
PUBLISHED: 2019, SOURCE: JOURNAL OF CYSTIC FIBROSIS, VOLUME: 18, ISSUE: 1
INDEXED IN: WOS
47
TITLE: Extent of rescue of F508de1-CFTR function by VX-809 and VX-770 in human nasal epithelial cells correlates with SNP rs7512462 in SLC26A9 gene in F508del/F508del Cystic Fibrosis patients Full Text
AUTHORS: Arthur Kmit; Fernando Augusto L Lima Marson; Stephanie Villa Nova Pereira; Adriana Mendes Vinagre; Gabriela Silva Leite; Maria Fatima Servidoni; Jose Dirceu Ribeiro; Antonio Fernando Ribeiro; Carmen Silvia Bertuzzo; Margarida Duarte Amaral;
PUBLISHED: 2019, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1865, ISSUE: 6
AUTHORS: Arthur Kmit; Fernando Augusto L Lima Marson; Stephanie Villa Nova Pereira; Adriana Mendes Vinagre; Gabriela Silva Leite; Maria Fatima Servidoni; Jose Dirceu Ribeiro; Antonio Fernando Ribeiro; Carmen Silvia Bertuzzo; Margarida Duarte Amaral;
PUBLISHED: 2019, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1865, ISSUE: 6
INDEXED IN: WOS
48
TITLE: Folding Status Is Determinant over Traffic-Competence in Defining CFTR Interactors in the Endoplasmic Reticulum Full Text
AUTHORS: Joao D Santos; Sara Canato; Ana S Carvalho; Hugo M Botelho; Kerman Aloria; Margarida D Amaral; Rune Matthiesen; Andre O Falcao; Carlos M Farinha;
PUBLISHED: 2019, SOURCE: CELLS, VOLUME: 8, ISSUE: 4
AUTHORS: Joao D Santos; Sara Canato; Ana S Carvalho; Hugo M Botelho; Kerman Aloria; Margarida D Amaral; Rune Matthiesen; Andre O Falcao; Carlos M Farinha;
PUBLISHED: 2019, SOURCE: CELLS, VOLUME: 8, ISSUE: 4
INDEXED IN: WOS
49
TITLE: Insight into the cellular effects of nitrated phospholipids: Evidence for pleiotropic mechanisms of action Full Text
AUTHORS: Sofia Duarte; Tania Melo; Rosario Domingues; Juan D de Dios Alche; Dolores Perez Sala;
PUBLISHED: 2019, SOURCE: FREE RADICAL BIOLOGY AND MEDICINE, VOLUME: 144
AUTHORS: Sofia Duarte; Tania Melo; Rosario Domingues; Juan D de Dios Alche; Dolores Perez Sala;
PUBLISHED: 2019, SOURCE: FREE RADICAL BIOLOGY AND MEDICINE, VOLUME: 144
INDEXED IN: Scopus WOS
50
TITLE: Inhibition of calpain 1 restores plasma membrane stability to pharmacologically rescued Phe508del-CFTR variant
AUTHORS: Ana M Matos; Francisco R Pinto; Patricia Barros; Margarida D Amaral; Rainer Pepperkok; Paulo Matos;
PUBLISHED: 2019, SOURCE: JOURNAL OF BIOLOGICAL CHEMISTRY, VOLUME: 294, ISSUE: 36
AUTHORS: Ana M Matos; Francisco R Pinto; Patricia Barros; Margarida D Amaral; Rainer Pepperkok; Paulo Matos;
PUBLISHED: 2019, SOURCE: JOURNAL OF BIOLOGICAL CHEMISTRY, VOLUME: 294, ISSUE: 36
INDEXED IN: Scopus WOS