51
TITLE: Plasma total and free fatty acids composition in human non-alcoholic steatohepatitis  Full Text
AUTHORS: De Almeida, IT; Cortez Pinto, H; Fidalgo, G; Rodrigues, D; Camilo, ME;
PUBLISHED: 2002, SOURCE: CLINICAL NUTRITION, VOLUME: 21, ISSUE: 3
INDEXED IN: Scopus WOS
IN MY: ORCID
52
TITLE: Complete beta-oxidation of valproate: cleavage of 3-oxovalproyl-CoA by a mitochondrial 3-oxoacyl-CoA thiolase
AUTHORS: Silva, MFB ; Ruiter, JPN; Overmars, H; Bootsma, AH; van Gennip, AH; Jakobs, C; Duran, M; de Alemida, IT; Wanders, RJA;
PUBLISHED: 2002, SOURCE: BIOCHEMICAL JOURNAL, VOLUME: 362, ISSUE: 3
INDEXED IN: Scopus WOS
IN MY: ORCID
53
TITLE: Complete β-oxidation of valproate: cleavage of 3-oxovalproyl-CoA by a mitochondrial 3-oxoacyl-CoA thiolase
AUTHORS: Margarida F.B SILVA; Jos P.N RUITER; Henk OVERMARS; Albert H BOOTSMA; Albert H van GENNIP; Cornelis JAKOBS; Marinus DURAN; Isabel TAVARES de ALMEIDA; Ronald J.A WANDERS;
PUBLISHED: 2002, SOURCE: Biochem. J. - Biochemical Journal, VOLUME: 362, ISSUE: 3
INDEXED IN: CrossRef
IN MY: ORCID
54
TITLE: Plasma total and free fatty acids composition in human non-alcoholic steatohepatitis  Full Text
AUTHORS: TAVARES DE ALMEIDA, I; CORTEZ-PINTO, H; FIDALGO, G; RODRIGUES, D; M.E CAMILO;
PUBLISHED: 2002, SOURCE: Clinical Nutrition, VOLUME: 21, ISSUE: 3
INDEXED IN: CrossRef
IN MY: ORCID
55
TITLE: Molecular genetic analysis of the cystathionine beta-synthase gene in Portuguese homocystinuria patients: three novel mutations. Letter to the Editor  Full Text
AUTHORS: Castro, R ; Heil, SG; Rivera, I ; Jakobs, C; de Almeida, IT; Blom, HJ;
PUBLISHED: 2001, SOURCE: CLINICAL GENETICS, VOLUME: 60, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
56
TITLE: Glycerol increases the yield and activity of human phenylalanine hydroxylase mutant enzymes produced in a prokaryotic expression system  Full Text
AUTHORS: Leandro, P ; Lechner, MC; de Almeida, IT; Konecki, D;
PUBLISHED: 2001, SOURCE: MOLECULAR GENETICS AND METABOLISM, VOLUME: 73, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
57
TITLE: Synthesis and intramitochondrial levels of valproyl-coenzyme A metabolites  Full Text
AUTHORS: Silva, MFB ; Ruiter, JPN; IJlst, L; Allers, P; ten Brink, HJ; Jakobs, C; Duran, M; de Almedia, IT; Wander, RJA;
PUBLISHED: 2001, SOURCE: ANALYTICAL BIOCHEMISTRY, VOLUME: 290, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
58
TITLE: Quantitative analysis of urinary acylglycines for the diagnosis of beta-oxidation defects using GC-NCI-MS  Full Text
AUTHORS: Costa, CG; Guerand, WS; Struys, EA; Holwerda, U; ten Brink, HJ; de Almeida, IT; Duran, M; Jakobs, C;
PUBLISHED: 2000, SOURCE: JOURNAL OF PHARMACEUTICAL AND BIOMEDICAL ANALYSIS, VOLUME: 21, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
59
TITLE: Dynamic changes of plasma acylcarnitine levels induced by fasting and sunflower oil challenge test in children
AUTHORS: Costa, CCG; De Almeida, IT; Jakobs, C; Poll The, BT; Duran, M;
PUBLISHED: 1999, SOURCE: PEDIATRIC RESEARCH, VOLUME: 46, ISSUE: 4
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
60
TITLE: Quantitative analysis of plasma acylcarnitines using gas chromatography chemical ionization mass fragmentography
AUTHORS: Costa, CG; Struys, EA; Bootsma, A; tenBrink, HJ; Dorland, L; deAlmeida, IT; Duran, M; Jakobs, C;
PUBLISHED: 1997, SOURCE: JOURNAL OF LIPID RESEARCH, VOLUME: 38, ISSUE: 1
INDEXED IN: Scopus WOS
IN MY: ORCID
Page 6 of 7. Total results: 66.