11
TITLE: Complete β-oxidation of valproate: cleavage of 3-oxovalproyl-CoA by a mitochondrial 3-oxoacyl-CoA thiolase
AUTHORS: Margarida F.B SILVA; Jos P.N RUITER; Henk OVERMARS; Albert H BOOTSMA; Albert H van GENNIP; Cornelis JAKOBS; Marinus DURAN; Isabel TAVARES de ALMEIDA; Ronald J.A WANDERS;
PUBLISHED: 2002, SOURCE: Biochem. J. - Biochemical Journal, VOLUME: 362, ISSUE: 3
INDEXED IN: CrossRef
13
TITLE: Synthesis and intramitochondrial levels of valproyl-coenzyme A metabolites  Full Text
AUTHORS: Silva, MFB ; Ruiter, JPN; IJlst, L; Allers, P; ten Brink, HJ; Jakobs, C; Duran, M; de Almedia, IT; Wander, RJA;
PUBLISHED: 2001, SOURCE: ANALYTICAL BIOCHEMISTRY, VOLUME: 290, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef
14
TITLE: Lactic acidosis in long-chain fatty acid beta-oxidation disorders  Full Text
AUTHORS: Ventura, FV; Ruiter, JPN; Ijlst, L; De Almeida, IT; Wanders, RJA;
PUBLISHED: 1998, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 21, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 22
15
TITLE: Carnitine palmitoyltransferase II specificity towards beta-oxidation intermediates - Evidence for a reverse carnitine cycle in mitochondria  Full Text
AUTHORS: Ventura, FV; Ijlst, L; Ruiter, J; Ofman, R; Costa, CG; Jakobs, C; Duran, M; De Almeida, IT ; Bieber, LL; Wanders, RJA;
PUBLISHED: 1998, SOURCE: EUROPEAN JOURNAL OF BIOCHEMISTRY, VOLUME: 253, ISSUE: 3
INDEXED IN: Scopus WOS CrossRef
16
TITLE: Valproate inhibits the mitochondrial pyruvate-driven oxidative phosphorylation in vitro  Full Text
AUTHORS: Silva, MFB ; Ruiter, JPN; IJlst, L; Jakobs, C; Duran, M; deAlmeida, IT; Wanders, RJA;
PUBLISHED: 1997, SOURCE: 34th Annual Meeting of the Society-for-the-Study-of-Inborn-Errors-of-Metabolism in JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 20, ISSUE: 3
INDEXED IN: Scopus WOS CrossRef: 34
17
TITLE: Inhibitory effect of 3-hydroxyacyl-CoAs and other long-chain fatty acid beta-oxidation intermediates on mitochondrial oxidative phosphorylation
AUTHORS: Ventura, FV; Ruiter, JPN; Ijlst, L; deAlmeida, IT ; Wanders, RJA;
PUBLISHED: 1996, SOURCE: 33rd Annual Meeting of the Society-for-the-Study-of-Inborn-Errors-of-Metabolism in JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 19, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef
18
TITLE: INHIBITION OF OXIDATIVE-PHOSPHORYLATION BY PALMITOYL-COA IN DIGITONIN-PERMEABILIZED FIBROBLASTS - IMPLICATIONS FOR LONG-CHAIN FATTY-ACID BETA-OXIDATION DISORDERS  Full Text
AUTHORS: VENTURA, FV; RUITER, JPN; IJLST, L; ALMEIDA, IT; WANDERS, RJA;
PUBLISHED: 1995, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1272, ISSUE: 1
INDEXED IN: Scopus WOS
19
TITLE: Inhibition of oxidative phosphorylation by palmitoyl-CoA in digitonin permeabilized fibroblasts: implications for long-chain fatty acid β-oxidation disorders  Full Text
AUTHORS: Fátima V Ventura; Jos P.N Ruiter; Lodewijk IJlst; Isabel T Almeida; Ronald J.A Wanders;
PUBLISHED: 1995, SOURCE: Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, VOLUME: 1272, ISSUE: 1
INDEXED IN: CrossRef
Page 2 of 2. Total results: 19.