Gustavo Tiscornia
AuthID: R-001-069
11
TITLE: Coenzyme Q(10) partially restores pathological alterations in a macrophage model of Gaucher disease
AUTHORS: de la Mata, M; Cotan, D; Oropesa Avila, M; Villanueva Paz, M; de Lavera, I; Alvarez Cordoba, M; Luzon Hidalgo, R; Suarez Rivero, JM; Tiscornia, G; Sanchez Alcazar, JA;
PUBLISHED: 2017, SOURCE: ORPHANET JOURNAL OF RARE DISEASES, VOLUME: 12, ISSUE: 1
AUTHORS: de la Mata, M; Cotan, D; Oropesa Avila, M; Villanueva Paz, M; de Lavera, I; Alvarez Cordoba, M; Luzon Hidalgo, R; Suarez Rivero, JM; Tiscornia, G; Sanchez Alcazar, JA;
PUBLISHED: 2017, SOURCE: ORPHANET JOURNAL OF RARE DISEASES, VOLUME: 12, ISSUE: 1
12
TITLE: Induced pluripotent stem cell modeling of Gaucher’s disease: What have we learned?
AUTHORS: Santos, DM; Tiscornia, G;
PUBLISHED: 2017, SOURCE: International Journal of Molecular Sciences, VOLUME: 18, ISSUE: 4
AUTHORS: Santos, DM; Tiscornia, G;
PUBLISHED: 2017, SOURCE: International Journal of Molecular Sciences, VOLUME: 18, ISSUE: 4
13
TITLE: Ear wound regeneration in the African spiny mouse Acomys cahirinus. Spiny Mouse Regeneration
AUTHORS: Dino Matias Santos; Ana Martins Rita; Ignasi Casanellas; Adelia Brito Ova; Ines Maria Araujo ; Deborah Power ; Gustavo Tiscornia;
PUBLISHED: 2016, SOURCE: REGENERATION, VOLUME: 3, ISSUE: 1
AUTHORS: Dino Matias Santos; Ana Martins Rita; Ignasi Casanellas; Adelia Brito Ova; Ines Maria Araujo ; Deborah Power ; Gustavo Tiscornia;
PUBLISHED: 2016, SOURCE: REGENERATION, VOLUME: 3, ISSUE: 1
14
TITLE: Mitochondrial Dysfunction in Lysosomal Storage Disorders
AUTHORS: Mario De la Mata; David Cotán; Marina Villanueva-Paz; Isabel De Lavera; Mónica Álvarez-Córdoba; Raquel Luzón-Hidalgo; Juan Suárez-Rivero; Gustavo Tiscornia; Manuel Oropesa-Ávila;
PUBLISHED: 2016, SOURCE: Diseases, VOLUME: 4, ISSUE: 4
AUTHORS: Mario De la Mata; David Cotán; Marina Villanueva-Paz; Isabel De Lavera; Mónica Álvarez-Córdoba; Raquel Luzón-Hidalgo; Juan Suárez-Rivero; Gustavo Tiscornia; Manuel Oropesa-Ávila;
PUBLISHED: 2016, SOURCE: Diseases, VOLUME: 4, ISSUE: 4
15
TITLE: pH-Responsive Pharmacological Chaperones for Rescuing Mutant Glycosidases Full Text
AUTHORS: Teresa Mena-Barragán; Aya Narita; Dino Matias; Gustavo Tiscornia; Eiji Nanba; Kousaku Ohno; Yoshiyuki Suzuki; Katsumi Higaki; José Manuel Garcia Fernández; Carmen Ortiz Mellet;
PUBLISHED: 2015, SOURCE: Angewandte Chemie International Edition - Angew. Chem. Int. Ed., VOLUME: 54, ISSUE: 40
AUTHORS: Teresa Mena-Barragán; Aya Narita; Dino Matias; Gustavo Tiscornia; Eiji Nanba; Kousaku Ohno; Yoshiyuki Suzuki; Katsumi Higaki; José Manuel Garcia Fernández; Carmen Ortiz Mellet;
PUBLISHED: 2015, SOURCE: Angewandte Chemie International Edition - Angew. Chem. Int. Ed., VOLUME: 54, ISSUE: 40
16
TITLE: Corrigendum to neuronopathic gaucher's disease: Induced pluripotent stem cells for disease modelling and testing chaperone activity of small compounds [Human Molecular Genetics 22, 4, (2013) 633-645] DOI: 10.1093/hmg/dds471
AUTHORS: Tiscornia, G; Vivas, EL; Matalonga, L; Berniakovich, I; Monasterio, MB; Eguizabal, C; Gort, L; Gonzalez, F; Mellet, CO; Fernandez, JMG; Ribes, A; Veiga, A; Belmonte, JCI;
PUBLISHED: 2014, SOURCE: Human Molecular Genetics, VOLUME: 23, ISSUE: 1
AUTHORS: Tiscornia, G; Vivas, EL; Matalonga, L; Berniakovich, I; Monasterio, MB; Eguizabal, C; Gort, L; Gonzalez, F; Mellet, CO; Fernandez, JMG; Ribes, A; Veiga, A; Belmonte, JCI;
PUBLISHED: 2014, SOURCE: Human Molecular Genetics, VOLUME: 23, ISSUE: 1
INDEXED IN: 
Scopus
Scopus17
TITLE: Neuronopathic Gaucher's disease: Induced pluripotent stem cells for disease modelling and testing chaperone activity of small compounds
AUTHORS: Tiscornia, G; Lorenzo Vivas, E; Matalonga, L; Berniakovich, I; Barragan Monasterio, M; Eguizabal, C; Gort, L; Gonzalez, F; Ortiz mellet, C; Garcia Fernandez, JM; Ribes, A; Veiga, A; Izpisua Belmonte, JC;
PUBLISHED: 2013, SOURCE: Human Molecular Genetics, VOLUME: 22, ISSUE: 4
AUTHORS: Tiscornia, G; Lorenzo Vivas, E; Matalonga, L; Berniakovich, I; Barragan Monasterio, M; Eguizabal, C; Gort, L; Gonzalez, F; Ortiz mellet, C; Garcia Fernandez, JM; Ribes, A; Veiga, A; Izpisua Belmonte, JC;
PUBLISHED: 2013, SOURCE: Human Molecular Genetics, VOLUME: 22, ISSUE: 4
18
TITLE: Modelling long QT syndrome with iPS cells: Be still, my beating heart .
AUTHORS: Tiscornia, G; Monserrat, N; Belmonte, JCI;
PUBLISHED: 2011, SOURCE: Circulation Research, VOLUME: 108, ISSUE: 6
AUTHORS: Tiscornia, G; Monserrat, N; Belmonte, JCI;
PUBLISHED: 2011, SOURCE: Circulation Research, VOLUME: 108, ISSUE: 6
19
TITLE: Diseases in a dish: Modeling human genetic disorders using induced pluripotent cells Full Text
AUTHORS: Tiscornia, G; Vivas, EL; Belmonte, JCI;
PUBLISHED: 2011, SOURCE: Nature Medicine, VOLUME: 17, ISSUE: 12
AUTHORS: Tiscornia, G; Vivas, EL; Belmonte, JCI;
PUBLISHED: 2011, SOURCE: Nature Medicine, VOLUME: 17, ISSUE: 12
20
TITLE: MicroRNAs in embryonic stem cell function and fate
AUTHORS: Tiscornia, G; Izpisua Belmonte, JC;
PUBLISHED: 2010, SOURCE: Genes and Development, VOLUME: 24, ISSUE: 24
AUTHORS: Tiscornia, G; Izpisua Belmonte, JC;
PUBLISHED: 2010, SOURCE: Genes and Development, VOLUME: 24, ISSUE: 24
