11
TITLE: The blood-brain barrier is disrupted in Machado-Joseph disease/spinocerebellar ataxia type 3: evidence from transgenic mice and humanpost-mortemsamples
AUTHORS: Lobo, DD; Nobre, RJ ; Miranda, CO ; Pereira, D; Castelhano, J; Sereno, J; Koeppen, A; Castelo Branco, M; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: ACTA NEUROPATHOLOGICA COMMUNICATIONS, VOLUME: 8, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 17
12
TITLE: Trehalose alleviates the phenotype of Machado-Joseph disease mouse models  Full Text
AUTHORS: Santana, MM; Paixao, S; Cunha Santos, J; Silva, TP; Trevino Garcia, A; Gaspar, LS; Nobrega, C ; Nobre, RJ ; Cavadas, C ; Greif, H; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: JOURNAL OF TRANSLATIONAL MEDICINE, VOLUME: 18, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 23
13
TITLE: Blood-brain barrier dysfunction as a neuropathological feature in Machado-Joseph Disease: results from human and mouse samples
AUTHORS: Diana Lobo; Rui Nobre ; Catarina Miranda ; Dina Pereira; João Castelhano; José Sereno; Miguel Castelo-Branco; Luís De Almeida ;
PUBLISHED: 2019, SOURCE: Frontiers in Cellular Neuroscience, VOLUME: 13
INDEXED IN: CrossRef
14
TITLE: Intersection of exosome secretion and autophagy on alpha-synuclein spreading profile in Parkinson’s disease cell models
AUTHORS: Rita Perfeito ; Vanessa Anjos; Andreia Marques; Rui Nobre ; Manuel Garrido; Jens Schwamborn; Luís De Almeida;
PUBLISHED: 2019, SOURCE: Frontiers in Cellular Neuroscience, VOLUME: 13
INDEXED IN: CrossRef
15
TITLE: Non-invasive and allele-specific silencing therapy for Polyglutamine disorders: the case of Machado-Joseph disease/Spinocerebellar ataxia type 3
AUTHORS: Rui Nobre ; Joana Saraiva; Susana Paixão; Cellia Fusco; Magda Santana; Catarina Miranda ; Lorena Petrella; Jose Sereno; Joao Castelhano; Miguel Castelo-Branco; Miguel Sena-Esteves; Luis Pereira De ALmeida ;
PUBLISHED: 2019, SOURCE: Frontiers in Cellular Neuroscience, VOLUME: 13
INDEXED IN: CrossRef
16
TITLE: Gene Therapies for Polyglutamine Diseases
AUTHORS: Matos, CA; Carmona, V; Vijayakumar, UG; Lopes, S; Albuquerque, P; Conceicao, M; Nobre, RJ ; Nobrega, C ; de Almeida, LP ;
PUBLISHED: 2018, SOURCE: POLYGLUTAMINE DISORDERS, VOLUME: 1049
INDEXED IN: Scopus WOS CrossRef: 16
17
TITLE: Repeated Mesenchymal Stromal Cell Treatment Sustainably Alleviates Machado-Joseph Disease
AUTHORS: Miranda, CO ; Marcelo, A; Silva, TP; Barata, J; Vasconcelos Ferreira, A; Pereira, D; Nobrega, C ; Duarte, S ; Barros, I; Alves, J; Sereno, J; Petrella, LI; Castelhano, J; Paiva, VH; Paulo Rodrigues-Santos ; Alves, V; Nunes Correia, I; Nobre, RJ ; Gomes, C; Castelo Branco, M; de Almeida, LP ; ...More
PUBLISHED: 2018, SOURCE: MOLECULAR THERAPY, VOLUME: 26, ISSUE: 9
INDEXED IN: Scopus WOS CrossRef: 23
18
TITLE: Hypoxia mimetic induces lipid accumulation through mitochondrial dysfunction and stimulates autophagy in murine preadipocyte cell line  Full Text
AUTHORS: Marques, AP; Rosmaninho Salgado, J ; Estrada, M; Cortez, V; Nobre, RJ ; Cavadas, C ;
PUBLISHED: 2017, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS, VOLUME: 1861, ISSUE: 3
INDEXED IN: Scopus WOS CrossRef: 20
20
TITLE: Gephyrin Cleavage in In Vitro Brain Ischemia Decreases GABA(A) Receptor Clustering and Contributes to Neuronal Death  Full Text
AUTHORS: Joo T Costa; Miranda Mele; Marcio S Baptista; Joao R Gomes; Karsten Ruscher; Rui J Nobre ; Luis Pereira de Almeida; Tadeusz Wieloch; Carlos B Duarte;
PUBLISHED: 2016, SOURCE: MOLECULAR NEUROBIOLOGY, VOLUME: 53, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 8
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