91
TITLE: Neuropeptide Y Enhances Progerin Clearance and Ameliorates the Senescent Phenotype of Human Hutchinson-Gilford Progeria Syndrome Cells
AUTHORS: Aveleira, CA; Ferreira Marques, M; Cortes, L; Valero, J; Pereira, D; Pereira de Almeida, L ; Cavadas, C ;
PUBLISHED: 2020, SOURCE: JOURNALS OF GERONTOLOGY SERIES A-BIOLOGICAL SCIENCES AND MEDICAL SCIENCES, VOLUME: 75, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 14
92
TITLE: Protocol for the Characterization of the Cytosine-Adenine-Guanine Tract and Flanking Polymorphisms in Machado-Joseph Disease Impact on Diagnosis and Development of Gene-Based Therapies
AUTHORS: Lopes, SM; Faro, R; Lopes, MM; Onofre, I; Mendonca, N; Ribeiro, J; Januario, C; Nobre, RJ ; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: JOURNAL OF MOLECULAR DIAGNOSTICS, VOLUME: 22, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef: 1
93
TITLE: Simple and Fast SEC-Based Protocol to Isolate Human Plasma-Derived Extracellular Vesicles for Transcriptional Research
AUTHORS: Gaspar, LS; Santana, MM; Henriques, C; Pinto, MM; Ribeiro Rodrigues, TM; Girao, H ; Nobre, RJ ; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: Molecular Therapy - Methods and Clinical Development in MOLECULAR THERAPY-METHODS & CLINICAL DEVELOPMENT, VOLUME: 18
INDEXED IN: Scopus WOS CrossRef: 26 Handle
94
TITLE: The blood-brain barrier is disrupted in Machado-Joseph disease/spinocerebellar ataxia type 3: evidence from transgenic mice and humanpost-mortemsamples
AUTHORS: Lobo, DD; Nobre, RJ ; Miranda, CO ; Pereira, D; Castelhano, J; Sereno, J; Koeppen, A; Castelo Branco, M; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: ACTA NEUROPATHOLOGICA COMMUNICATIONS, VOLUME: 8, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 17
95
TITLE: Trehalose alleviates the phenotype of Machado-Joseph disease mouse models  Full Text
AUTHORS: Santana, MM; Paixao, S; Cunha Santos, J; Silva, TP; Trevino Garcia, A; Gaspar, LS; Nobrega, C ; Nobre, RJ ; Cavadas, C ; Greif, H; de Almeida, LP ;
PUBLISHED: 2020, SOURCE: JOURNAL OF TRANSLATIONAL MEDICINE, VOLUME: 18, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 23
96
TITLE: Blood-brain barrier dysfunction as a neuropathological feature in Machado-Joseph Disease: results from human and mouse samples
AUTHORS: Diana Lobo; Rui Nobre ; Catarina Miranda ; Dina Pereira; João Castelhano; José Sereno; Miguel Castelo-Branco; Luís De Almeida ;
PUBLISHED: 2019, SOURCE: Frontiers in Cellular Neuroscience, VOLUME: 13
INDEXED IN: CrossRef
97
TITLE: Cordycepin activates autophagy through AMPK phosphorylation to reduce abnormalities in Machado-Joseph disease models
AUTHORS: Marcelo, A; Brito, F; Carmo Silva, S; Matos, CA; Alves Cruzeiro, J; Vasconcelos Ferreira, A; Koppenol, R; Mendonca, L; de Almeida, LP ; Nobrega, C ;
PUBLISHED: 2019, SOURCE: HUMAN MOLECULAR GENETICS, VOLUME: 28, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 37
98
TITLE: Ibuprofen enhances synaptic function and neural progenitors proliferation markers and improves neuropathology and motor coordination in Machado-Joseph disease models
AUTHORS: Mendonça, LS; Nóbrega, C ; Tavino, S; Brinkhaus, M; Matos, C; Tomé, S; Moreira, R; Henriques, D; Kaspar, BK; Pereira de Almeida, L ;
PUBLISHED: 2019, SOURCE: Human molecular genetics, VOLUME: 28, ISSUE: 22
INDEXED IN: Scopus CrossRef: 27
99
TITLE: Machado-Joseph disease/spinocerebellar ataxia type 3: lessons from disease pathogenesis and clues into therapy
AUTHORS: Matos, CA; de Almeida, LP ; Nobrega, C ;
PUBLISHED: 2019, SOURCE: JOURNAL OF NEUROCHEMISTRY, VOLUME: 148, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef: 93
100
TITLE: Neural Stem Cells of Parkinson's Disease Patients Exhibit Aberrant Mitochondrial Morphology and Functionality
AUTHORS: Walter, J; Bolognin, S; Antony, PMA; Nickels, SL; Poovathingal, SK; Salamanca, L; Magni, S; Perfeito, R ; Hoel, F; Qing, XB; Jarazo, J; Arias Fuenzalida, J; Ignac, T; Monzel, AS; Gonzalez Cano, L; de Almeida, LP ; Skupin, A; Tronstad, KJ; Schwamborn, JC;
PUBLISHED: 2019, SOURCE: STEM CELL REPORTS, VOLUME: 12, ISSUE: 5
INDEXED IN: Scopus WOS CrossRef: 69
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