31
TITLE: Stability of Zn-Ni-TiO2 and Zn-TiO2 nanocomposite coatings in near-neutral sulphate solutions  Full Text
AUTHORS: Gomes, A ; Almeida, I; Frade, T; Tavares, AC;
PUBLISHED: 2012, SOURCE: JOURNAL OF NANOPARTICLE RESEARCH, VOLUME: 14, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef
32
TITLE: Phenylalanine hydroxylase deficiency: Molecular epidemiology and predictable BH4-responsiveness in South Portugal PKU patients  Full Text
AUTHORS: Isabel Rivera ; Dina Mendes; Angela Afonso; Madalena Barroso; Ruben Ramos; Patricia Janeiro; Anabela Oliveira; Ana Gaspar; Isabel Tavares de Almeida;
PUBLISHED: 2011, SOURCE: MOLECULAR GENETICS AND METABOLISM, VOLUME: 104, ISSUE: SUPPL.
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
33
TITLE: Inhibition of 3-methylcrotonyl-CoA carboxylase explains the increased excretion of 3-hydroxyisovaleric acid in valproate-treated patients  Full Text
AUTHORS: Paula B M Luís; Jos P Ruiter; Lodewijk IJlst; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F B Silva;
PUBLISHED: 2011, SOURCE: Journal of Inherited Metabolic Disease - J Inherit Metab Dis, VOLUME: 35, ISSUE: 3
INDEXED IN: CrossRef
IN MY: ORCID
34
TITLE: Valproic acid utilizes the isoleucine breakdown pathway for its complete β-oxidation  Full Text
AUTHORS: Paula B.M Luís; Jos P Ruiter; Rob Ofman; Lodewijk IJlst; Marco Moedas; Luísa Diogo; Paula Garcia; Isabel Tavares de Almeida; Marinus Duran; Ronald J Wanders; Margarida F.B Silva;
PUBLISHED: 2011, SOURCE: Biochemical Pharmacology, VOLUME: 82, ISSUE: 11
INDEXED IN: CrossRef
IN MY: ORCID
36
TITLE: 3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: initial presentation in a young adult.
AUTHORS: Reimao, S; Morgado, C; Almeida, IT; Silva, M ; Corte Real, H; Campos, J;
PUBLISHED: 2009, SOURCE: Journal of inherited metabolic disease, VOLUME: 32 Suppl 1
INDEXED IN: Scopus
37
TITLE: 3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: Initial presentation in a young adult  Full Text
AUTHORS: Reimao, S; Morgado, C; Almeida, IT; Silva, M; Corte Real, HC; Campos, J;
PUBLISHED: 2009, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 32, ISSUE: 1
INDEXED IN: WOS
39
TITLE: Valproic acid metabolism and its effects on mitochondrial fatty acid oxidation: A review  Full Text
AUTHORS: Silva, MFB ; Aires, CCP; Luis, PBM; Ruiter, JPN; IJist, L; Duran, M; Wanders, RJA; Tavares T de Almeida;
PUBLISHED: 2008, SOURCE: 44th Annual Symposium of the Society-for-the-Study-of-Inborn-Errors-of-Metabolism in JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31, ISSUE: 2
INDEXED IN: Scopus WOS CrossRef
IN MY: ORCID
40
TITLE: Valproic acid metabolites inhibit dihydrolipoyl dehydrogenase activity leading to impaired 2-oxoglutarate-driven oxidative phosphorylation  Full Text
AUTHORS: Paula B M Luis; Jos P N Ruiter; Catia C P Aires; Graca Soveral ; Isabel Tavares de Almelda; Marinus Duran; Ronald J A Wanders; Margarida F B Silva ;
PUBLISHED: 2007, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS, VOLUME: 1767, ISSUE: 9
INDEXED IN: Scopus WOS
IN MY: ORCID
Page 4 of 7. Total results: 66.