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TITLE: CFTR mutations altering CFTR fragmentation
AUTHORS: Kendra Tosoni; Michelle Stobbart; Diane M Cassidy; Andrea Venerando; Mario A Pagano; Simao Luz ; Margarida D Amaral ; Karl Kunzelmann ; Lorenzo A Pinna; Carlos M Farinha ; Anil Mehta;
PUBLISHED: 2013, SOURCE: BIOCHEMICAL JOURNAL, VOLUME: 449, ISSUE: 1
INDEXED IN: Scopus WOS CrossRef
4
TITLE: Rescuing Mutant CFTR: A Multi-task Approach to a Better Outcome in Treating Cystic Fibrosis
AUTHORS: Margarida D Amaral ; Carlos M Farinha ;
PUBLISHED: 2013, SOURCE: CURRENT PHARMACEUTICAL DESIGN, VOLUME: 19, ISSUE: 19
INDEXED IN: Scopus WOS CrossRef
6
TITLE: BAG-1 Stabilizes Mutant F508del-CFTR in a Ubiquitin-Like-Domain-Dependent Manner
AUTHORS: Filipa Mendes ; Carlos M Farinha ; Veronica Felicio; Paulo C Alves; Isabel Vieira; Margarida D Amaral ;
PUBLISHED: 2012, SOURCE: CELLULAR PHYSIOLOGY AND BIOCHEMISTRY, VOLUME: 30, ISSUE: 5
INDEXED IN: Scopus WOS CrossRef
7
TITLE: FOLDING, TRAFFIC AND KINETIC DEFECTS ACCOUNT FOR F508DEL-CFTR RETENTION IN THE ENDOPLASMIC RETICULUM  Full Text
AUTHORS: Farinha, CM ; King Underwood, J; Sousa, M; Da Paula, A; Williams, J; Hirst, S; Amaral, MD;
PUBLISHED: 2012, SOURCE: PEDIATRIC PULMONOLOGY, VOLUME: 47
INDEXED IN: WOS
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TITLE: LMTK2 facilitates CFTR endocytosis by phosphorylation at CFTR Ser-737 residue  Full Text
AUTHORS: Cunha da Luz, SC; Cihil, K; Thibodeau, PH; Brautigan, DL; Amaral, MD; Farinha, CM ; Swiatecka Urban, A;
PUBLISHED: 2012, SOURCE: 22nd IUBMB Congress/37th FEBS Congress in FEBS JOURNAL, VOLUME: 279
INDEXED IN: WOS
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TITLE: PHOSPHORYLATION OF CFTR SER-737 RESIDUE BY LMTK2 REGULATES CFTR ENDOCYTOSIS  Full Text
AUTHORS: Luz, SF; Cihil, K; Thibodeau, PH; Brautigan, DL; Amaral, MD; Farinha, CM ; Swiatecka Urban, A;
PUBLISHED: 2012, SOURCE: PEDIATRIC PULMONOLOGY, VOLUME: 47
INDEXED IN: WOS
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TITLE: Regulation of ENaC biogenesis by the stress response protein SERP1  Full Text
AUTHORS: Diana Faria; Nicolas Lentze; Joana Almaca; Simao Luz ; Luisa Alessio; Yuemin M Tian; Jose Paulo Martins; Pedro Cruz; Rainer Schreiber; Mandana Rezwan; Carlos Miguel Farinha ; Daniel Auerbach; Margarida D Amaral ; Karl Kunzelmann ;
PUBLISHED: 2012, SOURCE: PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY, VOLUME: 463, ISSUE: 6
INDEXED IN: Scopus WOS CrossRef
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