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TITLE: Systems Approaches to Unravel Molecular Function: High-content siRNA Screen Identifies TMEM16A Traffic Regulators as Potential Drug Targets for Cystic Fibrosis  Full Text
AUTHORS: Pinto, Madalena C.; Botelho, Hugo M.; Silva, Iris A. L.; Railean, Violeta; Neumann, Beate; Pepperkok, Rainer; Schreiber, Rainer; Kunzelmann, Karl; Amaral, Margarida D.;
PUBLISHED: 2022, SOURCE: JOURNAL OF MOLECULAR BIOLOGY, VOLUME: 434, ISSUE: 5
INDEXED IN: Scopus WOS
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TITLE: The SLC26A9 inhibitor S9-A13 provides no evidence for a role of SLC26A9 in airway chloride secretion but suggests a contribution to regulation of ASL pH and gastric proton secretion
AUTHORS: Jo, Sungwoo; Centeio, Raquel; Park, Jinhong; Ousingsawat, Jiraporn; Jeon, Dong Kyu; Talbi, Khaoula; Schreiber, Rainer; Ryu, Kunhi; Kahlenberg, Kristin; Somoza, Veronika; Delpiano, Livia; Gray, Michael A.; Amaral, Margarida D.; Railean, Violeta; Beekman, Jeffrey M.; Rodenburg, Lisa W.; Namkung, Wan; Kunzelmann, Karl;
PUBLISHED: 2022, SOURCE: FASEB JOURNAL, VOLUME: 36, ISSUE: 11
INDEXED IN: Scopus WOS
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TITLE: Drug Repurposing for Cystic Fibrosis: Identification of Drugs That Induce CFTR-Independent Fluid Secretion in Nasal Organoids  Full Text
AUTHORS: Rodenburg, Lisa W.; Delpiano, Livia; Railean, Violeta; Centeio, Raquel; Pinto, Madalena C.; Smits, Shannon M. A.; van der Windt, Isabelle S.; van Hugten, Casper F. J.; van Beuningen, Sam F. B.; Rodenburg, Remco N. P.; van der Ent, Cornelis K.; Amaral, Margarida D.; Kunzelmann, Karl; Gray, Michael A.; Beekman, Jeffrey M.; Amatngalim, Gimano D.;
PUBLISHED: 2022, SOURCE: INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, VOLUME: 23, ISSUE: 20
INDEXED IN: Scopus WOS
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TITLE: CyFi-MAP: an interactive pathway-based resource for cystic fibrosis  Full Text
AUTHORS: Pereira, C; Mazein, A; Farinha, CM; Gray, MA; Kunzelmann, K; Ostaszewski, M; Balaur, I; Amaral, MD; Falcao, AO;
PUBLISHED: 2021, SOURCE: SCIENTIFIC REPORTS, VOLUME: 11, ISSUE: 1
INDEXED IN: Scopus WOS
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TITLE: Regulation of TMEM16A by CK2 and Its Role in Cellular Proliferation  Full Text
AUTHORS: Madalena C Pinto; Rainer Schreiber; Joana Lerias; Jiraporn Ousingsawat; Aires Duarte; Margarida Amaral; Karl Kunzelmann;
PUBLISHED: 2020, SOURCE: CELLS, VOLUME: 9, ISSUE: 5
INDEXED IN: Scopus WOS
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TITLE: KLF4 Acts as a wt-CFTR Suppressor through an AKT-Mediated Pathway  Full Text
AUTHORS: Luis Sousa; Ines Pankonien; Luka A Clarke; Iris Silva; Karl Kunzelmann; Margarida D Amaral;
PUBLISHED: 2020, SOURCE: CELLS, VOLUME: 9, ISSUE: 7
INDEXED IN: Scopus WOS
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TITLE: Organoids as a personalized medicine tool for ultra-rare mutations in cystic fibrosis: The case of S955P and 1717-2A > G  Full Text
AUTHORS: Iris A L Silva; Tereza Dousova; Sofia Ramalho; Raquel Centeio; Luka A Clarke; Violeta Railean; Hugo M Botelho; Andrea Holubova; Iveta Valaskova; Jiunn Tyng Yeh; Tzyh Chang Hwang; Carlos M Farinha; Karl Kunzelmann; Margarida D Amaral;
PUBLISHED: 2020, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1866, ISSUE: 11
INDEXED IN: Scopus WOS
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TITLE: Assessment of Distinct Electrophysiological Parameters in Rectal Biopsies for the Choice of the Best Diagnosis/Prognosis Biomarkers for Cystic Fibrosis  Full Text
AUTHORS: Silva, IAL; Duarte, A; Marson, FAL; Centeio, R; Dousova, T; Kunzelmann, K; Amaral, MD;
PUBLISHED: 2020, SOURCE: FRONTIERS IN PHYSIOLOGY, VOLUME: 11
INDEXED IN: Scopus WOS
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TITLE: Compartmentalized crosstalk of CFTR and TMEM16A (ANO1) through EPAC1 and ADCY1  Full Text
AUTHORS: Lérias, J; Pinto, M; Benedetto, R; Schreiber, R; Amaral, M; Aureli, M; Kunzelmann, K;
PUBLISHED: 2018, SOURCE: Cellular Signalling, VOLUME: 44
INDEXED IN: Scopus
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